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KMID : 1195620080010040224
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Clinical and Experimental Otorhinolaryngology
2008 Volume.1 No. 4 p.224 ~ p.226
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Juvenile Paget’s Disease with Paranasal Sinus Aplasia
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Bae Ki-Beom
Kwon Jae-Hwan
Kim Young-Ho
Jung Tae-Young
Cho Joong-Hwan
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Abstract
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Juvenile Paget’s disease (JPD) is a rare skeletal disorder that’s characterized by bone demineralization and elevated levels of serum alkaline phosphatase. JPD involves the paranasal sinuses in extremely rare cases. We report here on a 25-month-old Asian male who was diagnosed of JPD associated with aplasia of the paranasal sinuses, but not the ethmoid sinuses. The patient was successfully treated by surgery and we undertook no medical intervention. This appears to be the first reported case of JPD associated with bilateral paranasal sinus aplasia.
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KEYWORD
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Paget disease of bone, Osteitis deformans, Paranasal sinuses, Paranasal sinus neoplasms
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